Rare association of cardiac conditionsÑprolonged QT intervals, T-wave abnormalities, relative bradycardia, and ventricular tachyarrhythmiasÑwith sensorineural deafness. Patients present with episodes of seizures, syncope, or sudden death precipitated by intense emotion, exercise, or loud noises. Cardiac component of disorder is autosomal dominant, and deafness component is autosomal recessive.